منابع مشابه
Ornithine carbamyl transferase in Reye's syndrome.
Serum levels of ornithine carbamyl transferase activities were determined in the acutely ill and convalescent Reye's syndrome patients and in their parents. Acutely ill Reye's syndrome patients had elevated levels of serum ornithine carbamyl transferase activities as compared to those in controls. The convalescent Reye's syndrome patients and their parents had normal levels of serum ornithine c...
متن کاملImbalance in ornithine metabolism in hepatomas of different growth rates as expressed in behavior of L-ornithine carbamyl transferase activity.
The behavior of ornithine carbamyl transferase activity (carbamylphosphate :1.-ornithine carbamyltransferase, EC 2.1 .3.3) was compared in proliferating normal liver (from developing rats and from partially hepatectomized rats) and in neoplastic liver (spectrum of hepatomas of different growth rates). The behavior of the liver enzyme in starved animals was also examined. The enzyme activity was...
متن کاملA signal sequence domain essential for processing, but not import, of mitochondrial pre-ornithine carbamyl transferase
Studies using deletion mutagenesis indicate that a processing recognition site lies proximal to the normal cleavage position between gln32 and ser33 of pre-ornithine carbamyl transferase (pOCT). pOCT cDNA was manipulated to delete codons specifying amino acids 22-30 of the signal sequence. The mutant precursor, designated pOCT delta 22-30, was imported to the matrix compartment by purified mito...
متن کاملStudy of carbamyl phosphate-ornithine transcarbamylase.
The enzyme carbamyl phosphate-ornithine transcarbamylase, which catalyzes the synthesis of citrulline from ornithine plus carbamyl phosphate, has been partially purified from rat liver by means of heat treatment and ethanol fractionation (1). Krebs et al. (2) were able to demonstrate the arsenolysis of citrulline in a number of tissues and, by using sheep liver mitochondria, were able to purify...
متن کاملLate onset ornithine carbamoyl transferase deficiency in males.
Six boys with ornithine carbamoyl transferase deficiency presenting in infancy or later childhood are described. There was wide variation in both the time of presentation and the symptoms, which may initially suggest a neurological, behavioural, or gastroenterological problem. Two patients died, as did two male siblings who were probably affected, but with early recognition of the hyperammonaem...
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ژورنال
عنوان ژورنال: Acta Chemica Scandinavica
سال: 1957
ISSN: 0904-213X
DOI: 10.3891/acta.chem.scand.11-1088b